Treatment options for cystic fibrosis

Treatment options for cystic fibrosis

Cystic fibrosis is a hereditary condition that affects the exocrine glands and leads to the production of excessively thick mucus that blocks the intestines, pancreatic ducts, and even bronchi. Unfortunately, there is no permanent cure for cystic fibrosis, but a range of treatments is available to reduce or prevent complications and control the symptoms of this condition. Depending on the patient’s needs, the doctors and healthcare professionals can set up a care plan. Also, to monitor the condition, regular appointments are crucial.

Effective treatments and care plans to deal with cystic fibrosis

Exercise
Physical activities like swimming, running, and playing football can help in clearing mucus from the patient’s lungs. Also, such activities will improve the patient’s overall physical strength. It is best to consult a physiotherapist who can give advice on the right physical activities and exercises depending on the patient’s health condition.

Medicines
Various medicines are available in the market to deal with cystic fibrosis, and these can be inhaled, swallowed, or injected according to the doctor’s instructions. Doctors can prescribe antibiotics to treat and prevent chest infections. Medicines are also available to make coughing easier and to make the mucus thin.

Some medications help in widening the airways, making breathing easier for the patient. It is advisable to take medicines only after consulting a doctor.

Proper diet
People with cystic fibrosis have to maintain a healthy diet with high nutritional value, as sometimes, digesting food and absorbing nutrients can become difficult due to the thick mucus. The dietician can guide the patient about the intake of proper nutrients and extra calories to prevent malnutrition.

Mineral and vitamin supplements, a high-calorie diet, and digestive enzymes can be helpful. If a person with cystic fibrosis is suffering from constipation problems, they can take laxatives according to the doctor’s instructions.

CPT (Chest physical therapy)
Excessive mucus in the chest and airways can cause troubled breathing for patients. Various airway clearance techniques (ACTs) are available to help the affected person breathe more comfortably. Such techniques help to reduce the risk of lung infections as well. Pounding or clapping on the chest and back can help to loosen the mucus and make sure that it can get out easily.

Some ACTs can be done at home with the help of a friend or family member. Also, electric chest clappers are now available to pull mucus away from the airways using vibrations.

Gene therapy
Medical studies have shown that a defective CFTR gene causes cystic fibrosis. Though CFTR modulators can help in fixing this gene, this treatment is not suitable for every patient. This gene therapy will only work for people with specific gene mutations.

Other than all these treatment options, doctors may also recommend a lung transplant. But this treatment is only recommended when no other medical treatment is successful in clearing the patient’s lungs.

Medical science is evolving and progressing with each passing day. It is possible that a permanent cure for cystic fibrosis will be invented in the future.